Anaesthesia in myotonia congenita Becker

Review

The algorithm is dedicated to a rare neurological disease, congenital recessive form of myotonia congenita Becker. The algorithm logically leads from the first contact with the patient through the entire perioperative period up to the potential discharge from the hospital. Takes into account all stages of the decision-making process with an emphasis on the key factors that can complicate the health condition of the patient and operating performance. The individual steps of the algorithm are logical and smoothly follow each other. In addition to the correct answers, it suggests a possible common mistakes and incorrect procedure. The specified model belongs among the typical clinical situation. A great advantage of the algorithm is the fact that it confronts the doctor with realistically created situations of rare, but serious, disease. It is possible at any time to "step back" from mistakes which would mean a serious complication in real situation, and it allows to learn and choose the correct procedure. In real life this is not possible. Another advantage of the algorithm is the theoretical information/note, which increases the level of knowledge about this rare disease.